Diagnostie Criteria for Neurofibromatosis

Six or more cafe au lait macules over 5 mm in greatest diameter in prepubertal individuals and over 15 mm in greatest diameter in postpubertal individuals Two or more neurofibromas of any type or one plexiform neuroma Freckling in the axillary or inguinal region Optic glioma

Two or more Lisch nodules (iris hamartomas)

Distinctive osseous lesion such as sphenoidal dysplasia or thinning of long bone cortex with or without pseudoarthrosis First-degree relative (parent, sibling, or offspring) with neurofibromatosis 1 by these criteria Diagnostic Criteria for Neurofibromatosis 2

Bilateral eighth nerve masses seen with appropriate imaging teehniques

First-degree relative with neurofibromatosis 2 and either unilateral eighth nerve mass or two of the following: neurofibroma, meningioma, glioma, schwannoma, and juvenile posterior subcapsular lenticular opacity

'28] , [29! and in 1941, Louis-Bar proposed that ataxia- telangiectasia should also be considered as one of the phakomatoses. During the last 50 years a wide variety of disorders, all of which are unusual and many of which lack dysplastic or neoplastic characteristics, have been considered to belong to this heterogeneous group of disorders. The major neurocutaneous syndromes are considered herein, and others are noted in T§M§.3,2.-1.

How To Deal With Rosacea and Eczema

How To Deal With Rosacea and Eczema

Rosacea and Eczema are two skin conditions that are fairly commonly found throughout the world. Each of them is characterized by different features, and can be both discomfiting as well as result in undesirable appearance features. In a nutshell, theyre problems that many would want to deal with.

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