Neurocutaneous Disorders

The neurocutaneous syndromes comprise a group of heterogeneous disorders characterized by dysplasia and a tendency to form tumors. y , y The CNS and skin are primarily involved, but other organ systems can be affected. Since the skin and nervous tissue originate from the same germ layer, the ectoderm, these disorders have been variously called congenital ectodermoses and congenital neuroectodermal dysplasias. Van der Hoeve believed that the ocular findings of neurofibromatosis and tuberous sclerosis were similar and suggested that they be classified together under the inappropriate term phakomatosis (Greek phakos: lentil, mole, or birthmark).y He later added von Hippel- Lindau disease and Sturge-Weber syndrome to this category,

TABLE 32-1 -- SELECTED NEUROCUTANEOUS SYNDROMES

Disease

Incontinentia pigmenti achromians (hypomelanosis of Ito)

Rendu-Osler-Weber disease

Waardenburg's syndrome (I) Waardenburg's syndrome (II)

Ataxia-telangiectasia

Chediak-Higashi syndrome Refsum's syndrome

Rothmond-Thomson syndrome

Rud's syndrome

Sjogren-Larsson syndrome Xeroderma pigmentosum

Fabry-Anderson disease

Incontinentia pigmenti (Bloch-Sulzberger syndrome)

How To Deal With Rosacea and Eczema

How To Deal With Rosacea and Eczema

Rosacea and Eczema are two skin conditions that are fairly commonly found throughout the world. Each of them is characterized by different features, and can be both discomfiting as well as result in undesirable appearance features. In a nutshell, theyre problems that many would want to deal with.

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